Juvenile nasopharyngeal angiofibromas (JNA) are a rare benign but locally aggressive vascular tumor. Epidemiology Juvenile nasopharyngeal angiofibromas. Introduction: Juvenile nasopharyngeal angiofibroma (NAJ) is a tumor with .. Acessos Cirúrgicos no Angiofibroma Nasofaríngeo Juvenil – Relato de caso e. Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally aggressive fibrovascular tumor arising from the posterolateral wall of the.

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Contrast enhanced MRIs are used to achieve avid enhancement with flow voids.

Angiofibroma nasofaríngeo juvenil

Direct intratumoral embolization of juvenile angiofibroma. Nasopharyngeal carcinoma Nasopharyngeal carcinoma. It shows very aggressive behavior due to local invasiveness and is associated with various symptoms. Intracranial juvenile nasopharyngeal angiofibroma. Diagnosis of JNA is made by complete history, clinical examination, radiography, nasal endoscopy and by using specialized imaging techniques such as arteriography, computer tomography and magnetic resonance imaging.

There are several classifications of JNA, 15,16 but that by Andrews—Fisch 10 is the most widespread in the literature. Edit article Share article View revision history. Salvage Surgery in the Treatment aangiofibroma Local Recurrences of Several surgical approaches have been utilized for the removal of nasopharyngeal angiofibromas, including transnasal, transpalatal, transzygomatic, and transcervical accesses, in addition to lateral rhinotomy and mid-facial degloving, with or without extension to the upper lip or concomitant craniotomy 9.

A comparative study of surgical approches. Advanced lesions with orbital and intracranial extension are difficult to treat and may recur often. Craniofacial resection of advanced juvenile nasopharyngeal angiofibroma.


Thus, early diagnosis, accurate staging and adequate treatment are essential in the management of this lesion. Nasal cavity, paranasal sinuses, nasopharynx Other tumors Nasopharyngeal angiofibroma Author: Angioribroma tumor originates in the lateral wall of the nasal cavity, close to the superior border of the sphenopalatine foramen. The genetic alterations observed more often involve sex chromosomes.

Surgery is the treatment of choice for JNA. SNES, angiofibrpma endoscopic surgery. Arterial embolization in the management of posterior epistaxis. Tumour of the respiratory system. In 34 patients, the primary tumour irrigation system came from the external carotid artery; in one case, the tumour was irrigated by circulation from only the internal carotid artery.

Nasopharyngeal angiofibroma

Please cite this article as: Other methods such as hormone therapy, radiotherapy and chemotherapy juevnil modalities are now used occasionally as complementary treatments. InFriedberg called it juvenile angiofibroma. Type I includes lesions fundamentally localized to the nasal cavity, paranasal sinus, nasopharynx, or pterygopalatine fossa. Symptoms of JNA depend on tumour location, size and extent.

We retrospectively analysed the clinical data from 43 patients with JNA surgically treated in our Department from until How to cite this article. Preoperative tumour embolisation promotes a better control of intraoperative bleeding and a possible reduction in tumour size.

Jyvenil presence of prominent flow voids lead to a salt and pepper appearance on most sequences and are characteristic 5,6. Biological distinctions between juvenile nasopharyngeal angiofibroma and vascular malformation: Maurice M, Milad M.

Evolution in the Treatment of Juvenile Nasopharyngeal Angiofibroma.

Pathology Outlines – Nasopharyngeal angiofibroma

Unable to process the form. J Laryngol Otol,pp. Proliferation, angiogenesis and hormonal markers in juvenile nasopharyngeal angiofibroma.


The other 17 patients underwent endoscopic surgery alone. New author database being installed, click here for details. CiteScore measures average citations received per document published. Improvements in surgical techniques are designed to shorten surgical time and thereby reduce patient morbidity. agniofibroma

Rhinology, 43pp. Given the short period of patient follow-up, there were only two relapses in one year.

Orphanet: Angiofibroma nasofar ngeo juvenil

Genetic alterations in juvenile nasopharyngeal angiofibromas. Case 5 Case 5. Endoscopic resection of JNA, alone or in combination with limited external approaches, is the treatment of choice for JNA in early stages; in certain centres with sufficient experience, JNA in advanced stages are anglofibroma intervened.

iuvenil Hippocrates first described this tumor in the 5 th century B. The main advantage of endoscopic surgery is the possibility of obtaining a broad view of the lesion and its anatomic relationship with adjacent structures, promoting more accurate, complete dissection and better control of bleeding 9,14, See staging of juvenile nasopharyngeal angiofibromas.

However, recurrence reflects an initial incomplete resection.

Patients numbers two and three see table due to the large size of the tumor was performed in the same section in two parts split in half. This feature may be helpful is differentiating from other more aggressive lesions.